Primary intestinal lymphangiectasia with massive abdominal lymphatic malformation requiring surgical debulking
نویسندگان
چکیده
منابع مشابه
Primary intestinal lymphangiectasia.
Primary intestinal lymphangiectasia (PIL) is a rare disease of intestinal lymphatics presenting with hypoproteinemia, bilateral lower limb edema, ascites, and protein losing enteropathy. We report a series of 4 children from Chennai, India presenting with anasarca, recurrent diarrhea, hypoproteinemia and confirmatory features of PIL on endoscopy and histopathology.
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Primary intestinal lymphangiectasia (PIL) is a rare disorder, especially in adults. It causes a local disruption of chylus transport and is part of the exudative gastroenteropathies. Conservative therapy includes dietary measures or somatostatin medication. Taking the differential diagnosis of PIL into consideration is a major challenge, since patients suffering from PIL may present with diarrh...
متن کاملprimary intestinal lymphangiectasia
primary intestinal lymphangiectasia (pil) is a rare disease of intestinal lymphatics presenting with hypoproteinemia, bilateral lower limb edema, ascites and protein-losing enteropathy. we report a case of pil in a 22 year old patient from tabriz, iran who presented with anasarca edema, recurrent diarrhea, hypoproteinemia and confirmatory features of pil on endoscopy and histopathology. therefo...
متن کاملPrimary intestinal lymphangiectasia (Waldmann's disease)
Primary intestinal lymphangiectasia (PIL), Waldmann's disease, is a rare disorder of unknown etiology characterized by dilated intestinal lacteals leading to lymph leakage into the small-bowel lumen and responsible for protein-losing enteropathy leading to lymphopenia, hypoalbuminemia and hypogammaglobulinemia. PIL is generally diagnosed before 3 years of age but may be diagnosed in older patie...
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Lymphatic malformations are congenital vascular malformations with lymphatic differentiation. Although the most common locations for lymphatic malformation are the neck and axilla, they can occur at several locations in the body including the abdomen. The abdominal location is rather rare and accounts for approximately 5% of all lymphatic malformation. Abdominal lymphatic malformation can arise...
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ژورنال
عنوان ژورنال: Journal of Pediatric Surgery Case Reports
سال: 2013
ISSN: 2213-5766
DOI: 10.1016/j.epsc.2013.10.014